Kardiyovasküler Bozukluklar

Yazarlar

Necla Kasımoğlu
Ayşe Gürol
https://orcid.org/0000-0002-7408-5428

Özet

Kardiyovasküler bozukluklar, çocuk ve ergenlerde önemli morbidite ve mortalite nedenleri arasında yer almakta olup konjenital ve edinsel faktörler bağlamında geniş bir yelpazede meydana gelmektedir. Konjenital kalp hastalıkları, doğumda mevcut olan yapısal anormalliklerle karakterizeyken ve genetik ya da çevresel faktörlerden kaynaklanırken; kapak hastalıkları darlık ve yetmezlik mekanizmalarıyla ciddi hemodinamik dengesizliklere yol açar. Kalp kasını doğrudan etkileyen kardiyomiyopatiler; dilate, hipertrofik, restriktif ve aritmojenik tipleriyle kalbin kasılma ve gevşeme yeteneğini, dolayısıyla pompa işlevini bozar. Enfektif endokardit, miyokardit ve perikardit gibi enfeksiyöz patolojiler endotel, miyokard ve perikard tabakalarında inflamasyon, ödem ve nekroza neden olarak hayati risk oluşturur. A grubu $\beta$-hemolitik streptokok farenjitinin yol açtığı akut romatizmal ateş, özellikle kapak yetersizliklerine ve kronik kalp hasarına zemin hazırlar. Orta büyüklükteki arterleri etkileyen sistemik bir vaskülit olan Kawasaki hastalığı ise yüksek ateş, döküntü ve koroner arter anevrizması gibi ağır komplikasyonlarla edinsel kalp rahatsızlıklarının gelişiminde kritik rol oynar. Tüm bu bozuklukların yönetiminde tıbbi ve cerrahi tedavilerin yanı sıra, hastaların yaşam kalitesini artırmaya yönelik fiziksel aktivite planlaması, sodyum ve sıvı kısıtlamalarını içeren diyet uygulamaları, yaşamsal bulguların takibi ve multidisipliner bakım yaklaşımları hayati önem taşımaktadır.

Cardiovascular disorders constitute significant causes of morbidity and mortality among children and adolescents, presenting through a wide spectrum of congenital and acquired conditions. Congenital heart diseases are characterized by structural abnormalities present at birth, stemming from genetic or environmental factors, whereas valvular diseases induce severe hemodynamic instability through stenosis and regurgitation mechanisms. Directly affecting the myocardium, cardiomyopathies impair the cardiac pumping function and volume capacity across dilated, hypertrophic, restrictive, and arrhythmogenic types. Infectious pathologies such as infective endocarditis, myocarditis, and pericarditis induce inflammation, edema, and necrosis in distinct cardiac layers, leading to life-threatening complications. Acute rheumatic fever, triggered by group A $\beta$-hemolytic streptococcal pharyngitis, causes active inflammation in heart tissues and leads to chronic valvular insufficiency. Kawasaki disease, a systemic vasculitis affecting medium-sized arteries, plays a critical role in acquired cardiac conditions with severe complications including prolonged high fever, strawberry tongue, rashes, and coronary artery aneurysms. Managing these complex disorders relies heavily on medical and surgical interventions, alongside comprehensive multidisciplinary approaches incorporating regular vital sign monitoring, physical activity regulation, dietary restrictions regarding sodium and fluid intake, and continuous patient follow-ups to optimize quality of life.

Referanslar

Liu Y, Chen S, Zühlke L, et al. Global birth prevalence of congenital heart defects 1970–2017: updated systematic review and meta-analysis of 260 studies. Int J Epidemiol. 2019;48(2):455-463. doi:10.1093/ije/dyz009

Wu W, He J, Shao X. Incidence and mortality trend of congenital heart disease at the global, regional, and national level, 1990–2017. Medicine (Baltimore). 2020;99(23):e20593. doi:10.1097/MD.0000000000020593

Zhao L, Chen L, Yang T, et al. Birth prevalence of congenital heart disease in China, 1980–2019: a systematic review and meta-analysis of 617 studies. Eur J Epidemiol. 2020;35(7):631-642. doi:10.1007/s10654-020-00653-0

Zimmerman M, Sable C. Congenital heart disease in low‐and‐middle‐income countries: Focus on sub‐Saharan Africa. Am J Med Genet Part C Semin Med Genet. 2020;184(1):36-46. doi:10.1002/ajmg.c.31769

Ertunç M, Aktaş E. The importance of family-centered care for children with congenital heart disease. Heal Care Acad J. Published online May 19, 2022. doi:10.52880/sagakaderg.1105262

Özdemir AA. Kalp ve Dolaşım Sistemi Hastalıkları. In: Aydın D, Aba YA, eds. Anne ve Çocuk Sağlığı. 1. İstanbul Tıp Kitapevleri; 2019:371-381.

Syamasundar P. Congenital Heart Defects – A Review. In: Congenital Heart Disease - Selected Aspects. InTech; 2012. doi:10.5772/27002

Çavuşoğlu H. Fiziksel Gelişim Bozukluğu İle Doğan Çocuk ve Hemşirelik Bakımı. In: Çocuk Sağlığı Hemşireliğ. 14th ed. Sistem Ofset Basımevi; 2022:149-179.

Kılıçarslan Törüner E, Büyükgönenç L. Kardivasküler Sistem Sorunu Olan Çocuk. In: Kılıçarslan Törüner E, Büyükgönenç L, eds. Çocuk Sağlığı Temel: Hemşirelik Yaklaşımları. Ankara Nobel Tıp Kitapevleri; 2017:338-362.

Sun R, Liu M, Lu L, Zheng Y, Zhang P. Congenital Heart Disease: Causes, Diagnosis, Symptoms, and Treatments. Cell Biochem Biophys. 2015;72(3):857-860. doi:10.1007/s12013-015-0551-6

Boyle L, Kelly MM. The School Age Child with Congenital Heart Disease. Am J Matern Nurs. 2015;40(1).

Selamet Tierney ES. The benefit of exercise in children with congenital heart disease. Curr Opin Pediatr. 2020;32(5):626-632. doi:10.1097/MOP.0000000000000942

Dolgun G, İnal S, Bozkurt G. Çocuklarda Dolaşım Sistemi Hastalıkları ve Hemşirelik Bakımı. In: Conk Z, Başbakkal Z, Yılmaz HB, Bolışık B, eds. Pediatri Hemşireliği. Akademisyen Kitapevi; 2018:401-425.

Lantin-Hermoso MR, Berger S, Bhatt AB, et al. The Care of Children With Congenital Heart Disease in Their Primary Medical Home. Pediatrics. 2017;140(5). doi:10.1542/peds.2017-2607

Üzel M. Kardiyovasküler Sistem. In: Vural F, Üzel M, eds. İnsan Anatomisi. Akademi Basın ve Yayıncılık; 2016:49-56.

Arslan A, Ünalmış D. Dolaşım Sistemi. In: Acer N, ed. Sağlık Bilimleri İçin Anatomi. 2. İstanbul Medikal Sağlık ve Yayıncılık; 2021:70-80.

Emirzeoğlu M. Dolaşım Sistemi. In: Şahin B, ed. Sağlık Bilimleri İçin Temel Anatomi. 1st ed. İstanbul Medikal Sağlık ve Yayıncılık; 2019:117-120.

Türkmen E. Kalp Hastalıkları. In: Çelik S, Yeşil ÖU, eds. Dahili ve Cerrahi Hastalıklar Hemşireliği. 3rd ed. Nobel Akademik Yayıncılık Eğitim ve Dnışmanlık; 2015:83-109.

Korkmaz FD. Yapısal Enfeksiyöz ve Enflamatuar Kalp Hastalıkları. In: Karadakovan A, Aslan FE, eds. Dahili ve Cerrahi Hastalıklarda Bakım. 5. Akademisyen Kitapevi; 2020:495-517.

Özdemir Z, Şenol Çelik S. Kalp kapak hastalıkları cerrahisi ve hemşirelik bakımı. Turkiye Klin J Surg Nurs-Special Top. 2018;4(1):26-34.

Akdemir N, Özer ZC. Kalbin Yapısal Hastalıkları ve Hemşirelik Bakımı. In: Akdemir N, Birol L, eds. İç Hastalıkları ve Hemşirelik Bakımı. 5th ed. Akademisyen Kitapevi; 2020:569-595.

Baman JR, Sekhon S, Flaherty JD. What Is Aortic Stenosis? Aortic. JAMA. 2022;327(10):103. doi:10.1016/j.jacc.2020.11.035

Grimard BH, Safford RE, Burns EL. Aortic Stenosis: Diagnosis and Treatment. Am Fam Physician. Published online 2016:371-378.

Solak H, Görmüş N, Solak TM, Görmüş IS. Kalp Hastalıkları ve Cerrahisi. Efil Yayınevi; 2011.

Canatar T. Kalp ve Büyük Damar Hastalıkları. In: Topal K, ed. Pediatrics. Nobel Tıp Kitapevleri; 2008:205-224.

Patibandla S, Heaton J, Azzam JS. Aortic Insufficiency. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/32491360

Akinseye OA, Pathak A, Ibebuogu UN. Aortic Valve Regurgitation: A Comprehensive Review. Curr Probl Cardiol. 2018;43(8):315-334. doi:10.1016/j.cpcardiol.2017.10.004

Dewaswala N, Chait R. Aortic Regurgitation. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/32310404

Wenn P, Zeltser R. Aortic Valve Disease. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/31194362

Mahmaljy H, Tawney A, Young M. Transcatheter Aortic Valve Replacement. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/28613729

Shah SN, Sharma S, Bossuah KA. Mitral Stenosis (Nursing). StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/33760552

Chaudhari SS, Chokkalingam Mani B. Mitral Valve Insufficiency. (StatPearls Yayıncılık, ed.; 2022. http://www.ncbi.nlm.nih.gov/pubmed/32491821

Harb SC, Griffin BP. Mitral Valve Disease: a Comprehensive Review. Curr Cardiol Rep. 2017;19(8). doi:10.1007/s11886-017-0883-5

Shah PM. Current concepts in mitral valve prolapse-Diagnosis and management. J Cardiol. 2010;56(2):125-133. doi:10.1016/j.jjcc.2010.06.004

Shah SN, Gangwani MK, Oliver TI. Mitral Valve Prolapse. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/29262039

Cevasco M, Shekar PS. Surgical management of tricuspid stenosis. Ann Cardiothorac Surg. 2017;6(3):275-282. doi:10.21037/acs.2017.05.14

Golamari R, Bhattacharya PT. Tricuspid Stenosis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/29763166

Mulla S, Asuka E, Siddiqui WJ. Tricuspid Regurgitation. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/30252377

Arsalan M, Walther T, Smith RL, Grayburn PA. Tricuspid regurgitation diagnosis and treatment. Eur Heart J. 2017;38(9):634-638. doi:10.1093/eurheartj/ehv487

Demirbağ R. Triküspit kapak yetersizliğinde tedavi Management of the tricuspid valve regurgitation. Ana do lu Kar di yol Derg. 2009;(1):43-49.

Dahou A, Levin D, Reisman M, Hahn RT. Anatomy and Physiology of the Tricuspid Valve. JACC Cardiovasc Imaging. 2019;12(3):458-468. doi:10.1016/j.jcmg.2018.07.032

Heaton J, Kyriakopoulos C. Pulmonic Stenosis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/32809585

Kervan Ü, Sert DE, Akdi M, Koçak C. Kalp Kapak Hastalıkları Kılavuzu. In: Diken Aİ, Erentürk S, Rabuş MB, Akar AR, Sargın M, Özatik MA, eds. Kalp Kapak Hastalıkları Kılavuzu. Türk Kalp ve Damar Cerrahisi Derneği; 2020:90-100.

Saji AM, Sharma S. Pulmonary Regurgitation. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/32491496

Polat C, Enç N. Heart Valve Diseases and Nursing Care. J Cardiovasc Nurs. 2015;6(1):42-57. doi:10.5543/khd.2015.004

Jarvis S. Cardiomyopathies 1: classification, pathophysiology and symptoms. Nurs Times. 2019;115(7):38-42.

Japp AG, Gulati A, Cook SA, Cowie MR, Prasad SK. The Diagnosis and Evaluation of Dilated Cardiomyopathy. J Am Coll Cardiol. 2016;67(25):2996-3010. doi:10.1016/j.jacc.2016.03.590

Şahan E, Tüfekcioğlu O. Of classification of cardiomyopathies. Turkiye Klin. 2015;7(1):15-17. doi:10.1016/0002-8703(75)90235-5

Weintraub RG, Semsarian C, Macdonald P. Dilated cardiomyopathy. Lancet. 2017;390(10092):400-414. doi:10.1016/S0140-6736(16)31713-5

Basit H, Brito D, Sharma S. Hypertrophic Cardiomyopathy. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/28613539

Firth J. Cardiology: hypertrophic cardiomyopathy. Clin Med (Northfield Il). 2019;19(1):61-63. doi:10.7861/clinmedicine.19-1-61

Ommen SR, Semsarian C. Hypertrophic cardiomyopathy: a practical approach to guideline directed management. Lancet. 2021;398(10316):2102-2108. doi:10.1016/S0140-6736(21)01205-8

Geske JB, Ommen SR, Gersh BJ. Hypertrophic Cardiomyopathy. JACC Hear Fail. 2018;6(5):364-375. doi:10.1016/j.jchf.2018.02.010

Lee TM, Hsu DT, Kantor P, et al. Pediatric Cardiomyopathies HHS Public Access. Circ Res. 2017;121(7):855-873. doi:10.1161/CIRCRESAHA.116.309386.Pediatric

Muchtar E, Blauwet LA, Gertz MA. Restrictive Cardiomyopathy: Genetics, Pathogenesis, Clinical Manifestations, Diagnosis, and Therapy. Circ Res. 2017;121(7):819-837. doi:10.1161/CIRCRESAHA.117.310982

Brieler J, Breeden MA, Tucker J. Cardiomyopathy: An Overview. Am Fam Physician. 2017;96(10):640-646. http://www.ncbi.nlm.nih.gov/pubmed/29431384

Brown KN, Pendela VS, Ahmed I, Diaz RR. Restrictive Cardiomyopathy. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/30725919

Seferović PM, Polovina M, Bauersachs J, et al. Heart failure in cardiomyopathies: a position paper from the Heart Failure Association of the European Society of Cardiology. Eur J Heart Fail. 2019;21(5):553-576. doi:10.1002/ejhf.1461

Vio R, Angelini A, Basso C, et al. Hypertrophic Cardiomyopathy and Primary Restrictive Cardiomyopathy: Similarities, Differences and Phenocopies. J Clin Med. 2021;10(9):1954. doi:10.3390/jcm10091954

Calkins H, Corrado D, Marcus F. Risk Stratification in Arrhythmogenic Right Ventricular Cardiomyopathy. Circulation. 2017;136(21):2068-2082. doi:10.1161/CIRCULATIONAHA.117.030792

Shah SN, Umapathi KK, Oliver TI. Arrhythmogenic Right Ventricular Cardiomyopathy. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/29262224

Murillo H, Restrepo CS, Marmol-Velez JA, et al. Infectious Diseases of the Heart: Pathophysiology, Clinical and Imaging Overview. RadioGraphics. 2016;36(4):963-983. doi:10.1148/rg.2016150225

Gupta A, Mendez MD. Endocarditis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/29763019

Simsek-Yavuz S, Akar AR, Aydogdu S, et al. Diagnosis, Treatment and Prevention of Infective Endocarditis: Turkish Consensus Report. Klimik Dergisi/Klimik J. 2019;32(Supp1):2-116. doi:10.5152/kd.2019.51

Yallowitz AW, Decker LC. Infectious Endocarditis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/32491573

Enç N, Uysal H. Kalbin Enfeksiyöz Hastalıkları. In: Enç N, ed. İç Hastalıkları ve Hemşireliği. 2. Nobel Tıp Kitapevleri; 2017:110-119.

Cahill TJ, Prendergast BD. Infective endocarditis. Lancet. 2016;387(10021):882-893. doi:10.1016/S0140-6736(15)00067-7

Rajani R, Klein JL. Infective endocarditis: A contemporary update. Clin Med (Northfield Il). 2020;20(1):31-35. doi:10.7861/clinmed.cme.20.1.1

Lampejo T, Durkin SM, Bhatt N, Guttmann O. Acute myocarditis: Aetiology, diagnosis and management. Clin Med (Northfield Il). 2021;21(5):E505-E510. doi:10.7861/clinmed.2021-0121

Kang M, An J. Viral Myocarditis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/29083732

Pandey S, Rajasurya V. Nonviral Myocarditis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/30725613

Al-Akchar M, Kiel J. Acute Myocarditis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/28722877

Demir AA, Savas Y. Kardiyak Enfeksiyonlar Miyokardit ve Enfektif Endokardit. Türk Radyoloji Semin. 2019;6(2):290-299. doi:10.5152/trs.2018.667

Duman D, Fakültesi ÜT, Bd ÇK. Çocuklarda miyokardit / miyoperikarditlerde güncel yaklaşım tanı , tedavi ve izlem. Mersin Univ Saglık Bilim Derg 2022;15(Özel. 2022;15:42-48.

Dababneh E, Siddique MS. Pericarditis. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/28613734

Akkaya S, Hazirolan T. Perikard Hastaliklari. Türk Radyoloji Semin. 2019;6(2):218-232. doi:10.5152/trs.2018.604

Chiabrando JG, Bonaventura A, Vecchié A, et al. Management of Acute and Recurrent Pericarditis. J Am Coll Cardiol. 2020;75(1):76-92. doi:10.1016/j.jacc.2019.11.021

Chiabrando JG, Bonaventura A, Vecchié A, et al. Management of Acute and Recurrent Pericarditis: JACC State-of-the-Art Review. J Am Coll Cardiol. 2020;75(1):76-92. doi:10.1016/j.jacc.2019.11.021

Imazio M, Gaita F, LeWinter M. Evaluation and treatment of pericarditis: A systematic review. JAMA - J Am Med Assoc. 2015;314(14):1498-1506. doi:10.1001/jama.2015.12763

Szczygielska I, Hernik E, Kołodziejczyk B, Gazda A, Maślińska M, Gietka P. Rheumatic fever – new diagnostic criteria. Reumatologia/Rheumatology. 2018;56(1):37-41. doi:10.5114/reum.2018.74748

Karthikeyan G, Guilherme L. Acute rheumatic fever. Lancet. 2018;392(10142):161-174. doi:10.1016/S0140-6736(18)30999-1

Carapetis JR, Beaton A, Cunningham MW, et al. Acute rheumatic fever and rheumatic heart disease. Nat Rev Dis Prim. 2016;2(1):15084. doi:10.1038/nrdp.2015.84

Arvind B, Ramakrishnan S. Rheumatic Fever and Rheumatic Heart Disease in Children. Indian J Pediatr. 2020;87(4):305-311. doi:10.1007/s12098-019-03128-7

Webb RH, Grant C, Harnden A. Acute rheumatic fever. BMJ. Published online July 14, 2015:h3443. doi:10.1136/bmj.h3443

Rhodes KL, Rasa MM, Yamamoto LG. Acute Rheumatic Fever: Revised Diagnostic Criteria. Pediatr Emerg Care. 2018;34(6):436-442. doi:10.1097/PEC.0000000000001511

Köksal AO, Gültekin Soylu A, Özdemir O. Acute Rheumatıc Fever. Turkish J Pediatr Dis. Published online October 26, 2015. doi:10.12956/tjpd.2015.182

Hedrich CM, Schnabel A, Hospach T. Kawasaki Disease. Front Pediatr. 2018;6. doi:10.3389/fped.2018.00198

Singh S, Jindal AK, Pilania RK. Diagnosis of Kawasaki disease. Int J Rheum Dis. 2018;21(1):36-44. doi:10.1111/1756-185X.13224

Agarwal S, Agrawal DK. Kawasaki disease: etiopathogenesis and novel treatment strategies. Expert Rev Clin Immunol. 2017;13(3):247-258. doi:10.1080/1744666X.2017.1232165

Owens AM, Plewa MC. Kawasaki Disease. StatPearls Publishing; 2022. http://www.ncbi.nlm.nih.gov/pubmed/30725848

McCrindle BW, Rowley AH, Newburger JW, et al. Diagnosis, Treatment, and Long-Term Management of Kawasaki Disease: A Scientific Statement for Health Professionals From the American Heart Association. Circulation. 2017;135(17). doi:10.1161/CIR.0000000000000484

Kurt CN, Ertuğrul T. Kawasaki Hastalığı. Klin Tıp Pediatr Derg. 2021;(January):14-17.

de Angelis G, Bobbo M, Paldino A, et al. Cardiomyopathies in children: Classification, diagnosis and treatment. Curr Opin Organ Transplant. 2020;25(3):218-230. doi:10.1097/MOT.0000000000000755

Rife E, Gedalia A. Kawasaki Disease: an Update. Curr Rheumatol Rep. 2020;22(10):75. doi:10.1007/s11926-020-00941-4

Newburger JW, Takahashi M, Burns JC. Kawasaki Disease. J Am Coll Cardiol. 2016;67(14):1738-1749. doi:10.1016/j.jacc.2015.12.073

Yayınlanan

5 Aralık 2022

Lisans

Lisans